Asploro Journal of Biomedical and Clinical Case Reports

Asploro Journal of Biomedical and Clinical Case Reports

Foli Agbeko^1,2*, Fidèle Comlan Dossou³, Mawouto Fiawoo^1,4, Elom Ounoo Takassi^1,4, Mawulolo Kossi Kato⁴, Mawuse Koffi Guédénon^1,4, Kokou Agbékogni Réné Segbedji^5,6, Djatougbé Ayaovi Elie Akolly^1,4, Magnoulelem N’Zonou⁷, Sollim Talboussouma⁶, Mazama Pakoudjare², Homba Daké Batalia³, Kokouvi Evenyo Abalo³, Edem Koffi Djadou^1,3, Kokou Nadiedjoa Douti^1,2, Adama Dodji Gbadoe^1,7, Yawo Dzayissé Atakouma^1,4, Didier Koffi Gnamey^1,4
1Département de Pédiatrie / Faculté des Sciences de la Santé, Université de Lomé, Lomé, Togo
²CHU Campus, Service de Pédiatrie, Lomé, Togo
³CHR Sokodé, Service de Pédiatrie, Sokodé, Togo
⁴CHU Sylvanus Olympio, Service de Pédiatrie, Lomé, Togo
⁵Département de Pédiatrie / Faculté des Sciences de la Santé, Université de Kara, Kara, Togo
⁶CHU Kara, Service de Pédiatrie, Kara, Togo
⁷Hôpital de Bè, Service de Pédiatrie, Lomé, Togo

Corresponding Author: Dr. Foli Agbeko ^{ORCID iD}
Address: 03 BP 30 434, Lomé, Togo.
Received date: 24 September 2021; Accepted date: 18 October 2021; Published date: 26 October 2021

Citation: Agbeko F, Dossou FC, Fiawoo M, Takassi EO, Guédénon MK, Segbedji KAR, Akolly DAE, N’Zonou M, Talboussouma S, Pakoudjare M, Batalia HD, Abalo KE, Djadou EK, Douti KN, Gbadoe AD, Atakouma YD, Gnamey DK. Congenital Constriction Band Syndrome: Clinical Study of Three Cases in Togo. Asp Biomed Clin Case Rep. 2021 Oct 26;4(3):170-78.

Copyright © 2021 Agbeko F, Dossou FC, Fiawoo M, Takassi EO, Guédénon MK, Segbedji KAR, Akolly DAE, N’Zonou M, Talboussouma S, Pakoudjare M, Batalia HD, Abalo KE, Djadou EK, Douti KN, Gbadoe AD, Atakouma YD, Gnamey DK. This is an open-access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium provided the original work is properly cited.

Keywords: Amniotic Band Syndrome, Constriction Ring, Limb Congenital Malformation, Togo

Abbreviations: CCBS: Congenital Constriction Band Syndrome; ABD: Amniotic Band Disease

Abstract

Introduction: Congenital constriction band syndrome (CCBS) or amniotic band syndrome is a complex set of congenital malformations, mainly affecting the limbs, but also the craniofacial and thoraco-abdominal region.
The Patients: The purpose of this work is to describe the clinical and diagnostic aspects of CCBS in Togo in relation to 03 clinical cases.
The Primary Diagnoses, Interventions, and Outcomes: The first case is characterized by an asymmetric bilateral superficial constriction groove of the lower limbs, pseudosyndactylias and synostosis of the tibia and fibula on X-ray. The second has a deep strangulation in the left arm with an amputation of the fingers associated with hypochromic skin lesions, poorly hemmed polylobal ear and skin growths. The latter characterized by persistent bridle, strangulation and ischemia downstream of that of the left wrist with postnatal amputation of the left hand.
Conclusion: The strengthening of antenatal diagnosis, the introduction of genetic counselling and the establishment of a national malformations register should make it possible to improve the management of cases of amniotic flange disease.