Congenital Constriction Band Syndrome: Clinical Study of Three Cases in Togo

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Congenital Constriction Band Syndrome: Clinical Study of Three Cases in Togo

Foli Agbeko1,2*, Fidèle Comlan Dossou3, Mawouto Fiawoo1,4, Elom Ounoo Takassi1,4, Mawuse Koffi Guédénon1,4, Kokou Agbékogni Réné Segbedji5,6, Djatougbé Ayaovi Elie Akolly1,4, Magnoulelem N’Zonou7, Sollim Talboussouma6, Mazama Pakoudjare2, Homba Daké Batalia3, Kokouvi Evenyo Abalo3, Edem Koffi Djadou1,3, Kokou Nadiedjoa Douti1,2, Adama Dodji Gbadoe1,7, Yawo Dzayissé Atakouma1,4, Didier Koffi Gnamey1,4
1Département de Pédiatrie / Faculté des Sciences de la Santé, Université de Lomé, Lomé, Togo
2CHU Campus, Service de Pédiatrie, Lomé, Togo
3CHR Sokodé, Service de Pédiatrie, Sokodé, Togo
4CHU Sylvanus Olympio, Service de Pédiatrie, Lomé, Togo
5Département de Pédiatrie / Faculté des Sciences de la Santé, Université de Kara, Kara, Togo
6CHU Kara, Service de Pédiatrie, Kara, Togo
7Hôpital de Bè, Service de Pédiatrie, Lomé, Togo

Corresponding Author: Dr. Foli Agbeko ORCID iD
Address: 03 BP 30 434, Lomé, Togo.
Received date: 24 September 2021; Accepted date: 18 October 2021; Published date: 26 October 2021

Citation: Agbeko F, Dossou FC, Fiawoo M, Takassi EO, Guédénon MK, Segbedji KAR, Akolly DAE, N’Zonou M, Talboussouma S, Pakoudjare M, Batalia HD, Abalo KE, Djadou EK, Douti KN, Gbadoe AD, Atakouma YD, Gnamey DK. Congenital Constriction Band Syndrome: Clinical Study of Three Cases in Togo. Asp Biomed Clin Case Rep. 2021 Oct 26;4(3):170-78.

Copyright © 2021 Agbeko F, Dossou FC, Fiawoo M, Takassi EO, Guédénon MK, Segbedji KAR, Akolly DAE, N’Zonou M, Talboussouma S, Pakoudjare M, Batalia HD, Abalo KE, Djadou EK, Douti KN, Gbadoe AD, Atakouma YD, Gnamey DK. This is an open-access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium provided the original work is properly cited.

Keywords: Amniotic Band Syndrome, Constriction Ring, Limb Congenital Malformation, Togo

Abbreviations: CCBS: Congenital Constriction Band Syndrome; ABD: Amniotic Band Disease

Abstract

Introduction: Congenital constriction band syndrome (CCBS) or amniotic band syndrome is a complex set of congenital malformations, mainly affecting the limbs, but also the craniofacial and thoraco-abdominal region.
The Patients: The purpose of this work is to describe the clinical and diagnostic aspects of CCBS in Togo in relation to 03 clinical cases.
The Primary Diagnoses, Interventions, and Outcomes: The first case is characterized by an asymmetric bilateral superficial constriction groove of the lower limbs, pseudosyndactylias and synostosis of the tibia and fibula on X-ray. The second has a deep strangulation in the left arm with an amputation of the fingers associated with hypochromic skin lesions, poorly hemmed polylobal ear and skin growths. The latter characterized by persistent bridle, strangulation and ischemia downstream of that of the left wrist with postnatal amputation of the left hand.
Conclusion: The strengthening of antenatal diagnosis, the introduction of genetic counselling and the establishment of a national malformations register should make it possible to improve the management of cases of amniotic flange disease.